Keywords
Buschke
Connectivopathy
How to Cite
Abstract
Buschke‘s Scleredema is a rare connective tissue disorder of unknown etiology that is characterized by excess acid mucopolysaccharide deposition in the dermis. Based on etiology, three types are described. Clinically, symmetrical cutaneous induration that progressively affects the neck area, face, thorax, back and limbs, sparing hands and feet, characterize it. Diagnosis is based on clinical presentation and the characteristic histopathological findings. No specific or effective treatment has been established, although the use of immunosuppressants, systemic and local steroids, as well as systemic treatment with psoralens and ultraviolet radiation has been described. In this article we present the case of a patient with Buschke‘s Type 2 Scleredema.References
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