Keywords
inflammatory pseudotumor
autoimmune pancreatitis
How to Cite
Abstract
IgG4 related disease is a systemic, inmunomediated entity of fibroinflammatory features and unknown etiology, capable of targeting any organ of the economy promoting its functional insufficiency. Organs frequently affected are: pancreas, gallbladder and coleducus, breast, salivary and lacrimal glands, among others. Clinical manifestations depend upon the organ involved. The exact global incidence is unknown but is estimated as low. The diagnosis is suspected upon clinical and radiologic features, and confirmed through the presence of typical histopathological patterns after ruling out other more frequent pathologies. Treatment is aimed at reducing or inhibiting the progression of fibrosis with the use of corticosteroids and inmunosuppresants. We present here the first registered case of IgG4 related disease in Paraguay.References
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