Abstract
Introducción: ANCA associated vasculitis are rare ,but can have devastating consequences if not diagnosed and treated in a timely manner. Diagnosis can be difficult and management generally requires a multidisciplinary team. EULAR managemente guidelines were published del 2016 , and outlines a series of reccomedations. The objective of this survey was to describe ANCA vascultis management by nefrologists and rheumatologists in Paraguay and compare them to current guidelines.
Methods: 10 question survey generated through Survey Monkey, based on key points/reccomendations outlined in the EULAR- ERA/EDTA guidelines. The surey was sent to adult rheumatologist and nephrologists registered with the Paraguayan Rheumatology Societies and the Paraguayan Nephrology Society. Answers were exported to Excel and analyzed with SPS.
Results: We had a 62 % participation rate. Most professionals (75%) obtain diagnostic biopsies. Renal biopsies were the most frequently obtained. Cyclophosphamide and Glucocorticoids were the most frequently used indcution treatment, and maintanance treatment varied according to specialty. Eighty percent of responants mantain treatment for at least 24 months.
Conclusion: ANCA associated vasculitis management by rheumatologist and nephrologist in Paraguay is in accordance to recommendations madeEULAR- ERA/EDTA management guidelines in 2016. Further studies are needed to determine reason for some of the differences encountered.
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